Treatment of Congenital Complete Atrioventricular Heart Block With Permanent Epicardial Pacemaker in Neonatal Lupus Syndrome

TANRIVERDİ S., Ulger Z., Bilgin B. S., KÜLTÜRSAY N., YALAZ M., ATAY Y., ...Daha Fazla

IRANIAN RED CRESCENT MEDICAL JOURNAL, cilt.17, sa.9, 2015 (SCI-Expanded) identifier identifier identifier

  • Yayın Türü: Makale / Tam Makale
  • Cilt numarası: 17 Sayı: 9
  • Basım Tarihi: 2015
  • Doi Numarası: 10.5812/ircmj.16200
  • Dergi Adı: IRANIAN RED CRESCENT MEDICAL JOURNAL
  • Derginin Tarandığı İndeksler: Science Citation Index Expanded (SCI-EXPANDED), Scopus
  • Anahtar Kelimeler: Heart Block, Neonatal Lupus Syndrome, Artificial Cardiac Pacemaker, Therapy
  • Manisa Celal Bayar Üniversitesi Adresli: Hayır

Özet

Introduction: Neonatal lupus syndrome (NLS) is a passively acquired autoimmune condition due to the transplacental passage of maternal anti-Ro/SSA and anti-La/SSB antibodies in mothers with systemic lupus erythematosus (SLE), and congenital complete heart block (CHB) is its most serious manifestation. Skin and hepatic involvement may occur in later infancy. Case Presentation: A term infant with fetal bradycardia, detected at the 23rd gestational age, was diagnosed with CHB due to NLS and was successfully treated with a permanent epicardial pacemaker. The patient was reported here due to rarity of the procedure in neonatal period. Conclusions: Mothers with SLE should be screened and closely followed up during pregnancy for the development of fetal atrioventricular (AV) block.