Percutaneous embolization of congenital portosystemic venous shunt in an infant with respiratory distress

ALKAN F., Düzgün F., YÜKSEL H., TARHAN S., COŞKUN Ş.

Turkish Journal of Pediatrics, cilt.60, sa.4, ss.456-459, 2018 (SCI-Expanded) identifier identifier

  • Yayın Türü: Makale / Tam Makale
  • Cilt numarası: 60 Sayı: 4
  • Basım Tarihi: 2018
  • Doi Numarası: 10.24953/turkjped.2018.04.019
  • Dergi Adı: Turkish Journal of Pediatrics
  • Derginin Tarandığı İndeksler: Science Citation Index Expanded (SCI-EXPANDED), Scopus, TR DİZİN (ULAKBİM)
  • Sayfa Sayıları: ss.456-459
  • Anahtar Kelimeler: Amplatzer vascular plug II, Persistent ductus venosus, Portosystemic venous shunt
  • Manisa Celal Bayar Üniversitesi Adresli: Evet

Özet

A 5-month-old boy with progressive respiratory distress was admitted to our hospital. Physical examination revealed mild tachypnea and retraction. The left main bronchus was found as severely collapsed between the right pulmonary artery and the descending aorta, on the bronchoscopic evaluation. Further evaluation revealed persistent ductus venosus (PDV). As in the fetal period the ductus venosus arises from the posterior aspect of the left portal vein, a PDV is considered another type of intrahepatic portosystemic shunt. Therefore, he was diagnosed with congenital portosystemic venous shunt, leading to persistent respiratory distress. The PDV was closed with Amplatzer vascular plug II, and then he had immediate clinical improvement. Congenital portosystemic venous shunts (CPSS) are rare vascular malformations associated with severe complications. Here we presented a case with progressive respiratory distress as a result of CPSS and rapid improvement after embolization.